• Present at birth
    • 0.3% neonates
  • Variant of Naevus Flammeus
  • Clinical
    • Flat red patch
    • Trigeminal Nerve distribution
    • Grows with child
    • Does not regress
  • Associated with Sturge-Weber syndrome
    • Port wine stain in distribution of 1st branch V
    • Vascular malformation of meninges
    • Intracerebral calcification
  • Treatment
    • Laser treatment
      • Pulsed Dye laser
        • 40-45% response after 5-25 treatments