Aetiology
- Congenital
- May result from an inflammatory large vessel arteritis – e.g. Kawasaki’s or Takayasu’s
Clinical
- Sx of lower leg / mesenteric / renal ischemia
Management
- Congenital → Surgical Mx
- If on-going inflammation → Repair not recommended as these pts do poorly
- But if disease is quiescent with a normal ESR → surgical repair OK